Implant supported prosthesis in an edentulous boy with Hypohidrotic Ectodermal Dysplasia - "A happy boy". Authors; Gjoerup,H1; Nyhuus,L2; Buhl,J3. 1) Center for Oral Health in Rare Conditions, Aarhus University Hospital 2) Prosthodontic Department, the Dental School, Aarhus University 3) Department of Oral and Maxillofacial Surgery, Aarhus University Hospital Aim It is the aim of the presentation to report the prostethic treatment of a boy with hypohidrotic ectodermal dysplasia, to report the rationale behind the choices of treatment modalities, and to report the outcome of treatment experienced by the patient and his family. Case presentation The boy was untreated until the age of 5 years. His oral functions were compromised in relation to speech and psychosocial aspects. In the following 6 years, he underwent prosthodontic treatment in three phases. 1. At the age of 5 years a set of complete dentures were made to enhance speech and social well-being. The lower denture was retained by 2 ball attachments. 2. At the age of 8 years the dentures were remade because of need for augmentation of vertical dimensions, better fit, and better aesthetics for an 8 year old with mixed dentition in the anterior region. 3. At the age of 10 years a new set of dentures were made. This time the upper denture was made as an overdenture supported and retained by 4 implants and a Dolder bar. The surgical procedure included bone grafting from the anterior ramus mandibulae. The boy's subjective judgement of his oral health has been registered. The boy and his family experience great improvement in the functioning as well as the comfort of his prosthesis after insertion of implants. Conclusion The prosthesis for edentulous boys with HED demand several adjustments and revisions, partly due to growth of the jaws, partly due to the psychosocial development of the child. The use of implant supported prosthesis seems to be a relevant treatment option in edentulous jaws of children with HED. The surgical procedure is more complicated in the upper jaw than in the lower. The short term results are good, objectively as well as subjectively. The long term stability of the implants has to be elucidated in the forthcoming years.
International Conference on the Multidisciplinary Management of Ectodermal Dysplasia and Severe Hypodontia. Ed09. Abstract Book, 2009